A Quick Guide to Pulmonary Fibrosis


Pulmonary fibrosis refers to scarring of the lungs. It’s a chronic degenerative disease which leads to shortness of breath and fatigue.

To help you explain the disease to others, we’ve put together a brief guide using information from the Pulmonary Fibrosis Trust.

What is pulmonary fibrosis and idiopathic pulmonary fibrosis?

Pulmonary fibrosis is an interstitial lung disease that worsens over time. There are many reasons why a person may develop the disease including smoking, the inhalation of non-organic dust, connective tissue diseases such as scleroderma and a family history of the disease. If there is no found cause for a patient’s pulmonary fibrosis, it’s referred to as idiopathic pulmonary fibrosis (IPF).

Scarring occurs in the air sacs called alveoli which are situated at the end of the branches of tubes in the lungs. When these are scarred, they are unable to inflate and deflate properly making it increasingly difficult for oxygen to reach the blood.

Explaining idiopathic pulmonary fibrosis to newly diagnosed patients. Find out more here. 

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  1. Pat Quinn says:

    It’s very unfortunate there is nothing new on ibf treatments. This is just unacceptable that all tgd hope you give us is a transplant and not every one can get this.

    • Tim Bossie says:

      We at PFNews know what you’re saying and do wish that more treatments were available. However, researchers continue to be baffled at this disease. It is a horrible illness for everyone.

  2. Elaine says:

    My Mom succumbed to her disease 8 years after the diagnosis. She did live “normally” up to about 8 mos before her decline. We still wonder what caused her to get it.
    She was a school teacher….dust from chalk??
    She was 81. We “forgot” she had it until the rapid decline the 8 mos before her passing. She was on 40 (!!!!) liters of oxygen the week of her death..

  3. Elizabeth Mcdonald says:

    I just found out I had pulmonary fibrosis .don’t know much about it .I just can’t seem to slow down it makes it hard to breathe when I walk fast

  4. I really fought slowing down and then I went on a trip in a mountainous area and had a flair up that caused me to be unable to walk. The emergency room doctors were puzzled and I was admitted to the hospital and a specialist was called.
    Elderly would describe my age and fortunately I did not have any significant health problems. Yes, I am slowed down. Do I like it? Sometimes I do because I now have the chance to read, write and reflect. I can’t change how my lungs work, however, I can change how I react to how my lungs work.

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