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Hypersensitive Pneumonitis Anyone? (Mimics IPF)
Fibrotic hypersensitivity pneumonitis is a complex interstitial lung disease that is not entirely understood. In its chronic and fibrotic form, hypersensitivity pneumonitis is one of the main mimickers of idiopathic pulmonary fibrosis (IPF). Distinguishing between these two conditions is challenging but is of particular clinical relevance. Two approved therapies are available for IPF, and a considerable number of clinical trials are now exploring newer pharmacological options. This impressive research effort is a consequence of new pathogenetic understanding, updated diagnostic criteria and a long history of pharmacological trials. Conversely, current knowledge gaps on pathogenesis of chronic hypersensitivity pneumonitis, coupled with lack of validated diagnostic criteria, make the management of this disease an unsolved clinical challenge. This also reflects the paucity of therapeutic clinical trials in this field. In this review, we describe the current evidence and the possible future options to approach this complex disease.
This abstract comes from: https://pubmed.ncbi.nlm.nih.gov/32415523/
About Me: So… After over two years of looking for answers and thinking I had a clear diagnosis of IPF and six chemo treatments for Non-Hodgkins DLBCL lung cancer: the team of doctors at Cedars Sinai in Los Angeles provided me this diagnosis. They will be treating me with Esbriet, and I am ever so thankful for the topic page on this medication. It gives me hope, and I feel comfortable with the idea of starting it. I have so many questions about this ‘immune disorder’ lung disease, which I won’t go into here, but more to the point: I wonder if anyone else has heard of it, been diagnosed or treated for same? Lacking any other source for information I will continue to read through information that comes through this PF news source. It has been a gold mine for me. Many Thanks.
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